1.
Clin Case Rep
; 6(7): 1241-1245, 2018 Jul.
Artigo
em Inglês
| MEDLINE
| ID: mdl-29988644
RESUMO
Cryopyrin-associated periodic syndrome (CAPS) is a monogenetic auto-inflammatory disorder with systemic manifestations. Innate immune system aberrance is seen in both CAPS and erythema nodosum and this case may point to a previously unknown association. In pediatric patients with EN and systemic features, the possibility of underlying CAPS should be considered.